PBLD – Table #12 Case Skeleton for a Patient with Sickle Cell Disease and Moyamoya for Pial Synangiosis Moderators:
نویسندگان
چکیده
Objectives: -Discuss and understand the anesthetic considerations for a patient with complicated sickle cell disease who is undergoing general anesthesia. -Discuss and understand the pathophysiology of moyamoya disease. -Discuss and understand the preoperative, intraoperative, and postoperative management of patients with moyamoya disease. -Discuss and understand the implications of general anesthesia in patients with sickle cell disease complicated by a history of TIA and/or CVA. -Discuss and understand the effects of general anesthesia on cerebral blood flow and cerebral physiology.
منابع مشابه
Moyamoya Disease in an 18-Month-Old Female Caucasian Complicated by Cerebral Hyperperfusion Syndrome Following Indirect Revascularization
BACKGROUND Cerebral hyperperfusion syndrome is a rare complication of indirect revascularization due to moyamoya disease, but has not been reported previously in the pediatric population. We present a case of an 18-month-old girl with moyamoya disease that was treated with bilateral pial synangiosis and had complications consistent with cerebral hyperperfusion syndrome. This case report discuss...
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PURPOSE To describe the angiographic changes accompanying the surgical treatment of moyamoya disease by pial synangiosis and to compare these changes with patient outcome. METHODS The preoperative and postoperative cerebral angiograms, MR images, and clinical records of 13 children treated with pial synangiosis for moyamoya disease were reviewed. RESULTS After synangiosis, 10 patients had s...
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AIM Many direct and indirect surgical intervention methods have been defined for the treatment of moyamoya disease. Indirect surgical procedures have been increasingly used. In this study, indirect surgical intervention methods especially used in combination with pial synangiosis were assessed together with other indirect methods. MATERIAL AND METHODS 11 patients who were treated with an indi...
متن کاملLong-term outcome in children with moyamoya syndrome after cranial revascularization by pial synangiosis.
OBJECT Moyamoya syndrome, a narrowing of the basal intracranial vessels accompanied by the development of a cloud of collateral "moyamoya" vasculature, causes cerebral ischemia and stroke. This study was undertaken to determine if a standardized neurosurgical revascularization procedure, pial synangiosis, conferred long-term benefit in pediatric patients. METHODS The authors reviewed the clin...
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Sickle cell disease (SCD) is a known inherited hemoglobin disorder featured by the presence of sickle shaped erythrocytes in the blood. It can cause cerebrovascular accident (CVA) in adults and children and is responsible for the majority of the strokes in children. Repeated blood transfusion are often required in an attempt to dilute blood thus reducing the risk of vaso-occlusion and stroke in...
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